Community Health Network

Ranked among the nation's most integrated healthcare systems, Community Health Network is Central Indiana's leader in providing convenient access to exceptional healthcare services, where and when patients need them—in hospitals, health pavilions, workplaces, schools and homes.

Explore Community


Health library

En Español

Usher Syndrome

What is Usher syndrome?

Usher syndrome is an inherited disorder that involves both a hearing impairment and a vision impairment called retinitis pigmentosa. Some people also have varying problems with balance.

Usher syndrome is passed from parents to their children genetically.

What are the different types of Usher syndrome?

There are three types of Usher syndrome:

  • US type 1 (US1) - characteristics include:
    • profoundly deaf from birth
    • do not usually benefit from hearing aids
    • severe balance problems
    • vision problems begin by age 10
    • blindness eventually occurs
  • US type 2 (US2) - characteristics include:
    • moderate to severe hearing problems
    • usually benefit from hearing aids
    • use speech to communicate
    • normal balance
    • retinitis pigmentosa begins in teenage years
  • US type 3 (US3) - characteristics include:
    • born with normal hearing
    • hearing problems develop in teenage years
    • near normal balance
    • deafness by late adulthood
    • retinitis pigmentosa begins around puberty
    • blindness by mid-adulthood

How is Usher syndrome diagnosed?

Special tests assist in the diagnosis of Usher syndrome, including:

  • electronystagmography (ENG) to detect balance problems
  • electroretinography (ERG) to detect retinitis pigmentosa

Treatment for Usher syndrome:

Specific treatment for Usher syndrome will be determined by your physician based on:

  • your age, overall health, and medical history
  • extent of the disease
  • your tolerance for specific medications, procedures, or therapies
  • expectations for the course of the disease
  • your opinion or preference

At present, there is no known cure for Usher syndrome. The best treatment, however, is early identification so that education programs can begin as soon as possible. Treatment may include:

  • adjustment counseling
  • career counseling
  • assistive devices, such as hearing aids
  • orientation and mobility training
  • communication services
  • independent living training
  • low vision services
  • auditory training

Click here to view the
Online Resources of Otolaryngology

Proud sponsor

  • Indiana Fever
  • Indianapolis Indians
  • Indiana Pacers
  • Ed Carpenter Racing
  • Indy Eleven
  • Indy Fuel

Health and wellness shopping

  • Wellspring Medical at Home for medical supplies and equipment
  • FigLeaf Boutique
  • Jasmine gift shop
  • Wellspring Pharmacy

More about shops